TY - CHAP M1 - Book, Section TI - Prune Belly (Eagle-Barrett) Syndrome A1 - Barlotta, Kevin S. A1 - Stack, Lawrence B. A1 - Knoop, Kevin J. A2 - Knoop, Kevin J. A2 - Stack, Lawrence B. A2 - Storrow, Alan B. A2 - Thurman, R. Jason PY - 2021 T2 - The Atlas of Emergency Medicine, 5e AB - Prune belly syndrome (PBS) is a congenital disorder characterized by a partial or complete lack of abdominal musculature, severe urinary tract abnormalities, and bilateral cryptorchidism. The syndrome is typically recognized at birth or by ultrasound in utero. Severe renal dysplasia resulting in end-stage renal disease (ESRD) occurs in 50% of patients. ESRD and its complications are the most common reason a patient with PBS comes to the ED. Patients with PBS are at higher risk for recurrent urinary tract infection (UTI), chronic constipation, splenic torsion, and midgut and cecal volvulus. SN - PB - McGraw-Hill CY - New York, NY Y2 - 2024/10/15 UR - accessemergencymedicine.mhmedical.com/content.aspx?aid=1181041120 ER -