TY - CHAP M1 - Book, Section TI - Cystic Fibrosis A1 - Iqbal, Sabah F. A1 - Pillai, Dinesh A1 - Brown, Kathleen M. A1 - Klein, Bruce L. A2 - Schafermeyer, Robert A2 - Tenenbein, Milton A2 - Macias, Charles G. A2 - Sharieff, Ghazala Q. A2 - Yamamoto, Loren G. PY - 2014 T2 - Strange and Schafermeyer's Pediatric Emergency Medicine, 4e AB - Cystic fibrosis (CF) is the most common, life-limiting, autosomal recessive disease among Caucasians in the United States.It occurs in approximately 1 in 3500 White births and is being diagnosed increasingly in non-Caucasians as well.1 (Fig. 38-1)Most patients with CF have the classic triad of manifestations: Chronic pulmonary diseaseMalabsorption due to pancreatic insufficiencyElevated concentrations of sweat sodium and chloride.2There is considerable individual variation in the clinical manifestations, severity, and course of the disease. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/11/12 UR - accessemergencymedicine.mhmedical.com/content.aspx?aid=1105682193 ER -