RT Book, Section A1 Barlotta, Kevin S. A1 Stack, Lawrence B. A1 Knoop, Kevin J. A2 Knoop, Kevin J. A2 Stack, Lawrence B. A2 Storrow, Alan B. A2 Thurman, R. Jason SR Print(0) ID 1181041120 T1 Prune Belly (Eagle-Barrett) Syndrome T2 The Atlas of Emergency Medicine, 5e YR 2021 FD 2021 PB McGraw-Hill PP New York, NY SN 9781260134940 LK accessemergencymedicine.mhmedical.com/content.aspx?aid=1181041120 RD 2024/10/06 AB Prune belly syndrome (PBS) is a congenital disorder characterized by a partial or complete lack of abdominal musculature, severe urinary tract abnormalities, and bilateral cryptorchidism. The syndrome is typically recognized at birth or by ultrasound in utero. Severe renal dysplasia resulting in end-stage renal disease (ESRD) occurs in 50% of patients. ESRD and its complications are the most common reason a patient with PBS comes to the ED. Patients with PBS are at higher risk for recurrent urinary tract infection (UTI), chronic constipation, splenic torsion, and midgut and cecal volvulus.