RT Book, Section
A1 Barlotta, Kevin S.
A1 Stack, Lawrence B.
A1 Knoop, Kevin J.
A2 Knoop, Kevin J.
A2 Stack, Lawrence B.
A2 Storrow, Alan B.
A2 Thurman, R. Jason
SR Print(0)
ID 1181041120
T1 Prune Belly (Eagle-Barrett) Syndrome
T2 The Atlas of Emergency Medicine, 5e
YR 2021
FD 2021
PB McGraw-Hill
PP New York, NY
SN 9781260134940
LK accessemergencymedicine.mhmedical.com/content.aspx?aid=1181041120
RD 2024/04/19
AB Prune  belly  syndrome  (PBS)  is  a  congenital  disorder  characterized  by  a  partial  or  complete  lack  of  abdominal  musculature,  severe  urinary  tract  abnormalities,  and  bilateral  cryptorchidism.  The  syndrome  is  typically  recognized  at  birth  or  by  ultrasound  in  utero.  Severe  renal  dysplasia  resulting  in  end-stage  renal  disease  (ESRD)  occurs  in  50%  of  patients.  ESRD  and  its  complications  are  the  most  common  reason  a  patient  with  PBS  comes  to  the  ED.  Patients  with  PBS  are  at  higher  risk  for  recurrent  urinary  tract  infection  (UTI),  chronic  constipation,  splenic  torsion,  and  midgut  and  cecal  volvulus.