RT Book, Section
A1 Iqbal, Sabah F.
A1 Pillai, Dinesh
A1 Brown, Kathleen M.
A1 Klein, Bruce L.
A2 Schafermeyer, Robert
A2 Tenenbein, Milton
A2 Macias, Charles G.
A2 Sharieff, Ghazala Q.
A2 Yamamoto, Loren G.
SR Print(0)
ID 1105682193
T1 Cystic Fibrosis
T2 Strange and Schafermeyer's Pediatric Emergency Medicine, 4e
YR 2014
FD 2014
PB McGraw-Hill Education
PP New York, NY
SN 978-0-07-182926-7
LK accessemergencymedicine.mhmedical.com/content.aspx?aid=1105682193
RD 2024/04/18
AB Cystic  fibrosis  (CF)  is  the  most  common,  life-limiting,  autosomal  recessive  disease  among  Caucasians  in  the  United  States.It  occurs  in  approximately  1  in  3500  White  births  and  is  being  diagnosed  increasingly  in  non-Caucasians  as  well.1  (Fig.  38-1)Most  patients  with  CF  have  the  classic  triad  of  manifestations:  Chronic  pulmonary  diseaseMalabsorption  due  to  pancreatic  insufficiencyElevated  concentrations  of  sweat  sodium  and  chloride.2There  is  considerable  individual  variation  in  the  clinical  manifestations,  severity,  and  course  of  the  disease.